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Coats' disease and bilateral cataract in a child with Turner syndrome: a case report.

Beby F, Roche O, Burillon C, Denis P

Department of Ophthalmology, Edouard Herriot Hospital, Lyon, France. francis.beby@libertysurf.fr

PURPOSE: To report the first case in which Coats' disease was observed with infantile cataract in a girl with Turner syndrome (TS). MATERIALS AND METHODS: We examined a 4-year-old female infant with TS who was referred with a diagnosis of leukocoria in the left eye. RESULTS AND DISCUSSION: Examination under anaesthesia revealed a bilateral punctate cataract and left eye fundus showed vascular retinal abnormalities typical of Coats' disease. Cryotherapy was performed on the telangiectatic vessels and the child was followed up for a period of 12 months. Despite cryotherapy resulting in regression of the peripheral exudates, an exudative maculopathy persisted with poor visual outcome. We suggest that Coats' disease should be considered as a rare ocular manifestation in TS.

Published 29 November 2005 in Graefes Arch Clin Exp Ophthalmol, 243(12): 1291-3.
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